REPORTE DE CASO DE: EVOLUCION ATIPICA DE ENCEFALITIS DE RASMUSSEN.
DOI:
https://doi.org/10.51437/nj.v30i1.422Palabras clave:
Estatus epileptico, Encefalitis de Rasmussen, Epilepsia parcial continuaResumen
Resumen (Español)
Introducción: La encefalitis de Rasmussen es una entidad severa y poco frecuente, que predomina en la infancia. Su etiología es desconocida. Se caracteriza por ser una enfermedad progresiva, y por afectar un hemisferio, en forma de epilepsia parcial continua farmacorresistente, y atrofia hemisférica unilateral. A largo plazo deja secuelas neurológicas, lo que conlleva a una discapacidad desde una edad temprana.
Materiales y Métodos: Es un artículo de caso, sobre la evolución de un paciente con Encefalitis de Rasmussen.
Resultados: Se reporta un paciente de 9 años con una evolución atípica de la enfermedad, quien ha estado libre de crisis en más de 2 años y en monoterapia con bajas dosis de medicación.
Conclusiones: El reconocimiento y manejo temprano de esta patología incide en pronostico y complicaciones de un paciente con encefalitis de Rasmussen.
Palabras clave: Estatus epilepticus; Encefalitis de Rasmussen; Epilepsia parcial continua
Abstract (English)
Introduction: Rasmussen encephalitis is a severe and rare entity that predominates in childhood. Its etiology is unknown. It is characterized by being a progressive disease, and by affecting one hemisphere, in the form of drug-resistant continuous partial epilepsy, and unilateral hemispheric atrophy. In the long term, it leaves neurological consequences, which leads to disability from an early age.
Materials and Methods: It is a case report, on the evolution of a patient with Rasmussen Encephalitis.
Results: A 9-year-old patient is reported with an atypical evolution of the disease, who has been seizure-free for more than 2 years and on monotherapy with low doses of medication.
Conclusions: Early recognition and management of this pathology affects the prognosis and complications of a patient with Rasmussen encephalitis.
Keywords: Status epilepticus; Rasmussen encephalitis; Epilepsy partialis continua
Resumo (Português)
Introdução: A encefalite de Rasmussen é uma entidade grave e rara que predomina na infância. Sua etiologia é desconhecida. Caracteriza-se por ser uma doença progressiva e por afetar um hemisfério, na forma de epilepsia parcial contínua resistente a medicamentos e atrofia hemisférica unilateral. A longo prazo deixa sequelas neurológicas, que levam à incapacidade desde cedo.
Materiais e Métodos: É um artigo de caso, sobre a evolução de um paciente com Encefalite de Rasmussen.
Resultados: É relatado um paciente de 9 anos com evolução atípica da doença, há mais de 2 anos sem crises e em monoterapia com baixas doses de medicação.
Conclusões: O reconhecimento e tratamento precoce desta patologia afeta o prognóstico e as complicações de um paciente com encefalite de Rasmussen.
Palavras-chave: Estado de mal epiléptico; encefalite de Rasmussen; Epilepsia parcial contínua
Citas
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