Congenital kyphoscoliosis with hemivertebra: a 14-case series and literature review
DOI:
https://doi.org/10.51437/nj.v31i2.419Palabras clave:
spine, congenital scoliosis, diagnosis, treatmentResumen
Background: Hemivertebra results from an anomaly in the development of the vertebral body and is a cause of congenital scoliosis. Objective: To describe our experience with the surgical correction of congenital kyphoscoliosis with hemivertebra and review the literature to guide its diagnosis and timely management. Material and methods: A retrospective case series study, from January 2006 to July 2017, was conducted by reviewing the medical records of patients under 14 years of age included. Results: The study included 14 patients aged 3 months to 13 years, with a mean age of 6.9 years, 78.6% were male. Follow-up ranged from 18 to 144 months. Two patients were lost to follow-up. Twenty-two hemivertebrae were documented, 10 in the thoracic spine (45.4%), six in the cervical spine (27.3%), and six in the lumbar spine (27.3%). The most common surgical procedure was hemivertebra resection along with instrumented fusion, the osteosynthesis material being removed from four patients at ≥2 years of follow-up. Three patients had none-neurological complications. Conclusion: Hemivertebra resection along with instrumented fusion is a safe and effective surgical procedure to prevent and correct spinal deformity. In addition to early diagnosis and treatment, adequate follow-up by a multidisciplinary team is needed for better results.
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